2-HG (sodium salt)
目录号: A13632
α-羟基戊二酸(2-HG)是一种α-羟基酸。它通常通过D-和L-2-羟基戊二酸脱氢酶被代谢成2-酮戊二酸,这些酶的突变会导致2-羟基戊二酸尿症,一种神经代谢性疾病。
Discription | a-Hydroxyglutaric acid (2-HG) is an a-hydroxy acid. It is normally metabolized to 2-oxoglutarate by D- and L-2-hydroxyglutarate dehydrogenases, and mutations in these enzymes cause 2-hydroxyglutaric aciduria, a neurometabolic disorder. |
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目录号 | A13632 |
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分子式 | C5H6O5.2Na |
分子量 | 192.1 |
CAS号 | 40951-21-1 |
SMILES | [O-]C(C(CCC([O-])=O)O)=O.[Na+].[Na+] |
其他名称 | 2-HG, 2-Hydroxyglutaric Acid, a-Hydroxyglutaric acid |
储存条件 | Store lyophilized at -20ºC, keep desiccated. |
Calculate the dilution required to prepare a stock solution. This equation is commonly abbreviated as: C1V1 = C2V2