(R)-3-Hydroxyisobutyric acid
目录号: A18801
(R)-3-羟基异丁酸是L-缬氨酸和胸腺嘧啶代谢途径中的一种中间体,对于诊断极为罕见的遗传代谢疾病3-羟基异丁酸尿症和甲基丙烯醛脱氢酶缺乏症具有重要作用。
Discription | (R)-3-Hydroxyisobutyric acid is an intermediate in the pathways of l-valine and thymine and plays an important role in the diagnosis of the very rare inherited metabolic diseases 3-hydroxyisobutyric aciduria and methylmalonic semialdehyde dehydrogenase deficiency. |
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目录号 | A18801 |
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分子式 | C4H8O3 |
分子量 | 104.1 |
CAS号 | 1910-47-0 |
SMILES | O=C(O)[C@H](C)CO |
储存条件 | Store lyophilized at -20ºC, keep desiccated. |
Calculate the dilution required to prepare a stock solution. This equation is commonly abbreviated as: C1V1 = C2V2